Extraskeletal presentation of Ewing’s Sarcoma
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Keywords

Primary Ewing’s Sarcoma
Reconstructive Surgery
Oncology
Pathology

How to Cite

Mangual, D., Bisbal-Matos, L. A., Jiménez-Lee, R., Vélez, R., & Noy, M. (2018). Extraskeletal presentation of Ewing’s Sarcoma. Puerto Rico Health Sciences Journal, 37(1), 55–57. Retrieved from https://prhsj.rcm.upr.edu/index.php/prhsj/article/view/1570

Abstract

The case of a 27-year-old Hispanic female who presented with an occipito-parietal tumor after suffering trauma to the area. A physical examination revealed no tenderness to palpation and with evidence of healing ulcerations. The biopsy was consistent with a synovial sarcoma. A wide excision of the mass (15cm x 14cm x 6cm) followed by a pericranial flap was performed. A follow-up CT showed recurrence involving the parietal sagittal sinus. After a second biopsy the mass was determined to be a small-cell sarcoma, consistent with Ewing’s sarcoma. Chemotherapy included 8 cycles of doxorubicin, vincristine, and cyclophosphamide, with alternating cycles of etoposide and ifosfamide. A year later, a second wide excision of the mass was performed, followed by bilaminate skin substitute and skin graft placement for reconstruction of the soft-tissue defect. After chemotherapy, a follow-up PET scan showed no signs of re-uptake in any soft tissue or skeletal structures. After 2 years, the patient remains in complete remission.
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